| Index | Gene Name Primary | Protein Name | Gene Name Synonym | Uniprot ID |
|---|---|---|---|---|
| 1 | ACACA | Acetyl-CoA carboxylase 1 | ACAC ACC1 ACCA | Q13085 |
| 2 | ACACB | Acetyl-CoA carboxylase 2 | ACC2 ACCB | O00763 |
| 3 | CAD | CAD protein [Includes: Glutamine-dependent carbamoyl-phosphate synthase | P27708 | |
| 4 | CPS1 | Carbamoyl-phosphate synthase [ammonia], mitochondrial | P31327 | |
| 5 | MCCC1 | Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial | MCCA | Q96RQ3 |
| 6 | PC | Pyruvate carboxylase, mitochondrial | P11498 | |
| 7 | PCCA | Propionyl-CoA carboxylase alpha chain, mitochondrial | P05165 |